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Patient-derived TWNK variants recapitulate multisystem Perrault syndrome pathology in a mouse mode
Author: Wang, Wei; Dong, Xiang; Cao, Chun-yu; Li, Hong-bo; Lv, Ya-feng
Journal: MITOCHONDRION. 2026; Vol. 88, Issue , pp. -. DOI: 10.1016/j.mito.2026.102137
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Mitochondrial dysfunction-induced PANoptosis: Mechanisms, triggers, and disease implication
Author: Pan, Liyang; Fang, Shijie; Kong, Fanhua; Ye, Shaojun; Xiong, Yan
Journal: MITOCHONDRION. 2026; Vol. 88, Issue , pp. -. DOI: 10.1016/j.mito.2026.102115
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PP2A inhibition alleviates DCD liver damage during prolonged cold ischemia by interfering Drp1 translocation and ER stres
Author: Lan, Jianan; Lu, Zhongshan; Cheng, Quanwei; Sun, Yujie; Ye, Shaojun; Xiong, Yan
Journal: MITOCHONDRION. 2026; Vol. 88, Issue , pp. -. DOI: 10.1016/j.mito.2026.102118
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Mitochondria transfer from myocytes to endothelial cells promotes angiogenesis in skeletal muscl
Author: Long, Yu-Feng; Huang, Ai-Jun; Tang, Shuo; Xu, Zhen; Wu, Ming-Yue; Liu, Kai; Chen, Ze-Cai; Qin, Lei; Dai, Bing-Yang; Dong, Cheng; Cheung, Wing-Hoi; Wang, Xin-Luan; Yang, Da-Zhi
Journal: MITOCHONDRION. 2026; Vol. 87, Issue , pp. -. DOI: 10.1016/j.mito.2026.102116
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Exogenous mitochondrial transfer alleviates neurodegeneration in Parkinson's disease model by improving mitochondrial functio
Author: Si, Yu; Hayat, Muhammad Abid; Ni, Yingyin; Zhang, Jingwen; Guo, Tao; Cao, Yudie; Hong, Yancheng; Zuo, Hao; Sun, Xin; Li, Zheng; Chen, Bo; Wan, Jia; Wang, Yong; Hu, Jiabo
Journal: MITOCHONDRION. 2026; Vol. 87, Issue , pp. -. DOI: 10.1016/j.mito.2026.102111
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Biallelic FOXRED1 mutations cause infantile mitochondrial encephalopathy with complex I disassembly and basal ganglia degeneratio
Author: Pan, Cunhui; Zhu, Ruowei; Huang, Xi; Duan, Haolin; Wu, Tenghui; Wang, Xiaole; Ding, Ying; Chen, Chen; He, Fang; Peng, Jing; Yin, Fei; Lou, Xiaoting; Yang, Li
Journal: MITOCHONDRION. 2026; Vol. 87, Issue , pp. -. DOI: 10.1016/j.mito.2025.102110
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Aagab-driven SHIP2 degradation rescues mitochondrial dysfunction in hypoxic-ischemic encephalopath
Author: Han, Jinli; He, Lu; Chen, Ling; Wen, Bin; Ji, Jinglu
Journal: MITOCHONDRION. 2026; Vol. 87, Issue , pp. -. DOI: 10.1016/j.mito.2025.102109
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Targeting mitochondrial quality control for myocardial ischemia-reperfusion injur
Author: He, Yuxuan; Ren, Sixu; Liu, Chenglin; Zheng, Xiufen; Zhu, Cuilin
Journal: MITOCHONDRION. 2025; Vol. 84, Issue , pp. -. DOI: 10.1016/j.mito.2025.102046