Amyotrophic Lateral Sclerosis And Frontotemporal Degeneration

Amyotrophic Lateral Sclerosis And Frontotemporal Degeneration

肌萎缩侧索硬化和额颞叶变性

  • 3区 中科院分区
  • Q3 JCR分区

高引用文章

文章名称 引用次数
Primary lateral sclerosis: a distinct entity or part of the ALS spectrum? 21
Longitudinal structural changes in ALS: a three time-point imaging study of white and gray matter degeneration 18
Efficacy and tolerability of EH301 for amyotrophic lateral sclerosis: a randomized, double-blind, placebo-controlled human pilot study 17
The Swedish motor neuron disease quality registry 15
Safety and tolerability of Triumeq in amyotrophic lateral sclerosis: the Lighthouse trial 12
Amyotrophic lateral sclerosis in Nordland county, Norway, 2000-2015: prevalence, incidence, and clinical features 12
A novel D90_K91insN mutation in exon 4 of the SOD1 gene caused familial amyotrophic lateral sclerosis in a Chinese pedigree 12
Neurofilaments in pre-symptomatic ALS and the impact of genotype 12
ALS longitudinal studies with frequent data collection at home: study design and baseline data 11
Experience with telemedicine in a multi-disciplinary ALS clinic 11
Spanish adaptation of the edinburgh cognitive and behavioral amyotrophic lateral sclerosis screen (ECAS) 10
The project MinE databrowser: bringing large-scale whole-genome sequencing in ALS to researchers and the public 10
Split-hand index in amyotrophic lateral sclerosis: an F-wave study 9
Clinical characteristics of a large cohort of US participants enrolled in the National Amyotrophic Lateral Sclerosis (ALS) Registry, 2010-2015 9
ALS reversals: demographics, disease characteristics, treatments, and co-morbidities 8
Radicava (edaravone) for amyotrophic lateral sclerosis: US experience at 1 year after launch 8
Evaluation of remote pulmonary function testing in motor neuron disease 8
Mass spectrometry analysis of plasma from amyotrophic lateral sclerosis and control subjects 8
Reducing sample size requirements for future ALS clinical trials with a dedicated electrical impedance myography system 8
Screening for cognitive and behavioral change in amyotrophic lateral sclerosis/motor neuron disease: a systematic review of validated screening methods 8
Plasma creatinine and amyotrophic lateral sclerosis prognosis: a systematic review and meta-analysis 8
An epidemiologic investigation of amyotrophic lateral sclerosis in Thrace, Turkey, 2006-2010* 8
Defining pre-symptomatic amyotrophic lateral sclerosis 7
Loss of appetite is associated with a loss of weight and fat mass in patients with amyotrophic lateral sclerosis 7
Lunasin does not slow ALS progression: results of an open-label, single-center, hybrid-virtual 12-month trial 7
Epidemiology of amyotrophic lateral sclerosis in Friuli-Venezia Giulia, North-Eastern Italy, 2002-2014: a retrospective population-based study 7
Amyotrophic lateral sclerosis and food intake 7
Patterns of symptom development in patients with motor neuron disease 7
Unveiling early cortical and subcortical neuronal degeneration in ALS mice by ultra-high field diffusion MRI 7
The TiM system: developing a novel telehealth service to improve access to specialist care in motor neurone disease using user-centered design 7
Cognitive-behavioral longitudinal assessment in ALS: the Italian Edinburgh Cognitive and Behavioral ALS screen (ECAS) 7
Riluzole does not improve lifespan or motor function in three ALS mouse models 7
VITALITY-ALS, a phase III trial of tirasemtiv, a selective fast skeletal muscle troponin activator, as a potential treatment for patients with amyotrophic lateral sclerosis: study design and baseline characteristics 6
Trauma and amyotrophic lateral sclerosis: a european population-based case-control study from the EURALS consortium 6
Increase in DNA methylation in patients with amyotrophic lateral sclerosis carriers of not fully penetrant SOD1 mutations 6
A neuropsychological and behavioral study of PLS 6
Identification and functional analysis of novel mutations in the SOD1 gene in Chinese patients with amyotrophic lateral sclerosis 6
Provision of assistive technology devices among people with ALS in Germany: a platform-case management approach 6
Derivation of norms for the Dutch version of the Edinburgh cognitive and behavioral ALS screen 6
Early post-marketing experience with edaravone in an unselected group of patients with ALS 6
Relationship of statins and other cholesterol-lowering medications and risk of amyotrophic lateral sclerosis in the US elderly 5
The burden of apathy for caregivers of patients with amyotrophic lateral sclerosis 5
Risk factors for social withdrawal in amyotrophic lateral sclerosis/motor neurone disease 5
Loss of functional connectivity is an early imaging marker in primary lateral sclerosis 5
Primary progressive aphasia and the FTD-MND spectrum disorders: clinical, pathological, and neuroimaging correlates 5
A randomized controlled trial of resistance and endurance exercise in amyotrophic lateral sclerosis 5
Amyotrophic lateral sclerosis among patients with a Medicare Advantage prescription drug plan; prevalence, survival and patient characteristics 5
Measuring reliable change in cognition using the Edinburgh Cognitive and Behavioural ALS Screen (ECAS) 5
A spatial analysis of amyotrophic lateral sclerosis (ALS) cases in the United States and their proximity to multidisciplinary ALS clinics, 2013 5
Profile of medical care costs in patients with amyotrophic lateral sclerosis in the Medicare programme and under commercial insurance 5